鍔涘澶?鍒╅瞾鍞戠墖)鏄洰鍓嶆不鐤桝LS鐥囨渶
銆€銆€紜疄錛屽湪鐩墠榪樻病鏈夊摢浜涜嵂鐗╁湪娌葷枟鑲岃悗緙╀晶緔㈢‖鍖?ALS)鐥囨垨榪愬姩絏炵粡鍏冪柧鐥呯殑鐤楁晥涓婂彲浠ヨ秴榪囧姏濡傚お(鍒╅瞾鍞戠墖)錛岃€屼笖鍔涘澶繕鏄敮涓€寰楀埌緹庡浗FDA鎵瑰噯鐨勬不鐤楄倢钀庣緝渚х儲紜寲鐥囩殑鑽墿銆備絾鏄埌鐩墠涓烘紜疄榪樻湁涓€閮ㄥ垎鐨勫浗瀹舵病鏈夋壒鍑嗗姏濡傚お涓婂競錛屽師鍥犲叾瀹炲緢綆€鍗曪紝鍦ㄤ嬌鐢ㄥ墠錛屼嬌鐢ㄨ€呭繀欏繪敞鎰忎複搴婃湁鍏崇殑;杈圭紭鏀瑰杽紼嬪害鍜屾垚鏈枟鏁堟瘮闂銆?br />銆€銆€鐩墠錛屽嵆浣挎槸鍔涘澶?鍒╅瞾鍞戠墖)涔熶笉鑳芥牴闄よ倢钀庣緝渚х儲紜寲(ALS)鐥囷紝鍙槸寤剁紦鎮h€呯殑瀵垮懡銆傛垚鏈枟鏁堟瘮闂浣垮姞鎷垮ぇ鍜屾境澶у埄浜氫綔鍑轟笉鎵瑰噯鍔涘澶殑鍐沖畾錛岃繖鍦ㄨ嫳鍥戒篃閬囧埌鍚屾牱闂錛屼竴浜涘湴鏂瑰尰鐤楁満鏋勬嫆緇濈粰璿ヨ嵂鎻愪緵鍩洪噾錛岀敱姝ゆ垚浜嗘絳夊鏂矽嵂銆傝嫳鍥藉尰鐤楃粡嫻庡瀹惰綆楀彂鐜幫紝涓€涓倢钀庣緝渚х儲紜寲(ALS)鐥呬漢鐢ㄥ埄椴佸攽娌葷枟鐨勬湀璐圭敤涓?43鍀?86鑻遍晳錛屽勾鎬昏姳璐歸珮杈?5000鑻遍晳錛屾不鐤楁垚鏈お楂樸€傛鏄洜涓轟環鏍艱繃楂橈紝鑰屼笖鍔涘澶?鍒╅瞾鍞戠墖)涔熷彧鏄兘璧峰埌寤剁紦鐨勪綔鐢紝浣垮緢澶氫漢閮芥湜鑰屽嵈姝ワ紝鏀懼純浣跨敤鍔涘澶不鐤椼€?br />銆€銆€灝界浣跨敤鍔涘澶?鍒╅瞾鍞戠墖)娌葷枟鐨勬垚鏈珮錛岃€屼笖鍙兘寤剁紦鐤劇棶鍙戝睍錛屼絾鏄編鍥界緇忕棶瀛︾爺絀墮櫌璁や負鍒╅瞾鍞戝簲浠嬬粛緇欐墍鏈夌棶浜猴紝涓€欏圭編鍥借皟鏌ユ樉紺猴細鍚勪釜鑲岃悗緙╀晶緔㈢‖鍖?ALS)鐥囨不鐤椾腑蹇冧嬌鐢ㄥ埄椴佸攽鏈夊緢澶у樊璺濓紝鏈?8鍒?5涓嶇瓑鐨勭棶浜轟嬌鐢紝閫犳垚濡傛澶х殑宸窛涓昏鏄湪鍖葷敓涓帹騫誇笉澶熷拰鍖葷枟淇濋櫓闂銆傚湪鏀跺洖絳斿嵎鐨?59鍚嶅彈璋冩煡鐥呬漢涓紝9O%鐨勭棶浜虹О鍚榪囧埄椴佸攽,43%鐥呬漢縐扮敤榪囪鑽?240浜轟嬌鐢ㄨ€呭綋涓湁81浜哄凡緇忓仠鑽?鍋滆嵂鍘熷洜鏈夛細57浜鴻鏄壇浣滅敤闂錛?8浜鴻涓哄畠鐤楁晥涓嶅ソ錛?1浜鴻寰楀畠澶吹銆?br />銆€銆€涓€浣嶇編鍥藉鑰呮寚鍑猴細鎵€鏈夌粡浠栫殑鎵嬫帴鍙楁湰鍝佹不鐤楃殑鐥呬漢涓彧鏈変竴鍗婂喅瀹氱敤瀹冿紱鉶界劧鍔涘澶?鍒╅瞾鍞戠墖)榪樹笉鑳藉畬鍏ㄦ不鎰堣倢钀庣緝渚х儲紜寲(ALS)鐥囷紝鑰屼笖浠鋒牸鏄傝吹錛屼絾鏄粡榪囧騫寸殑鐮旂┒涔熻〃鏄庯紝鐩墠涓烘涔熷彧鏈夊姏濡傚お(鍒╅瞾鍞戠墖)鐨勭枟鏁堟渶濂姐€傞殢鐫€鍖誨鐨勫彂灞曪紝浣跨敤鍔涘澶?鍒╅瞾鍞戠墖)錛屽啀鑱斿悎鍏跺畠鑽墿娌葷枟蹇呭皢鍙栧緱鏇村ソ鐨勭枟鏁堬紝鑲岃悗緙╀晶緔㈢‖鍖栫棁(ALS)灝嗕笉鍐嶆槸緇濈棁銆?br />